Primitive neuroendocrine tumors (PNETs) are rare neoplasms
that are usually seen in children and frequently metastasis in
the central nervous system. At this setting, intramedullary, extramedullary,
intra-extramedullary and extradural have been
described. To our knowledge, only 25 cases of purely intramedullary
PNETs (IPNETs) have been previously reported.
We present a case of primary intrameduller PNET. The initial
treatment of the PNET is surgery and, if possible, the radical
extirpation of the tumour. Administration of radiotherapy and
chemotherapy appears to increase survival.
Keywords: Intrameduller primitive neuroendocrine tumor; chemotherapy; radiotherapy
